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Metastatic Pattern of Spread of Dermatofibrosarcoma Protuberans  adult

Introduction: Dermatofibrosarcoma Protruberans (DFSP) is a locally aggressive soft tissue sarcoma arising within the skin. Metastases are extremely rare, though local recurrence is common. A small subset (~10%) have a high-grade sarcoma component, which appears to raise the risk of recurrence or metastasis.

Lymphatic metastases are extremely rare. The lesion does invade adjacent structures, however, and MRI may be used to evaluate extent of disease preoperatively.

Prevalence: Very Rare Metastasis Frequency: Very Rare


Am J Surg Pathol. 1998;22(5):576. PMID 9591728

Primary Tumor:

 Characteristics Comments
Skin (Cutaneous and Subcutaneous) Plaque

Known Metastatic Locations:

SiteFrequencyCharacteristics Comments
Lung Parenchyma CommonNodule
Local Lymph Nodes Rare